ATPAF2 Antibody - Primary antibody, specific to ATPAF2, Rabbit IgG

Application:

Features and benefits

Item Number

Ab090208

Grouped product items
SKU	Size	Availability	Price
Ab090208-10μl	10μl	Available within 8-12 weeks(?) Production requires sourcing of materials. We appreciate your patience and understanding.	$69.90
Ab090208-50μl	50μl	Available within 8-12 weeks(?) Production requires sourcing of materials. We appreciate your patience and understanding.	$209.90
Ab090208-100μl	100μl	Available within 8-12 weeks(?) Production requires sourcing of materials. We appreciate your patience and understanding.	$319.90
Ab090208-1ml	1ml	Available within 8-12 weeks(?) Production requires sourcing of materials. We appreciate your patience and understanding.	$2,299.90

pAb; Rabbit anti Human ATPAF2 Antibody; WB; Unconjugated

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Basic Description

Product Name	ATPAF2 Antibody - Primary antibody, specific to ATPAF2, Rabbit IgG
Synonyms	ATP synthase mitochondrial F1 complex assembly factor 2antibody \| ATP12antibody \| ATP12 homologantibody \| ATP12pantibody \| LP3663antibody \| MC5DN1 antibody
Specifications & Purity	Validated, 1.0 mg/mL
Host species	Rabbit
Specificity	ATPAF2
Immunogen	A synthetic peptide derived from human ATPAF2 (AA 21-70)
Positive Control	WB: Jurkat and MCF7 cell lysates.
Conjugation	Unconjugated
Grade	Validated
Product Description	Rabbit anti Human ATPAF2 Antibody, Polyclonal, could be used for WB and so on. Application: WB: 1/500-1/2000 Relevance ATPAF2 belongs to the ATP12 family. It may play a role in the assembly of the F1 component of the mitochondrial ATP synthase (ATPase). Defects in ATPAF2 are the cause of complex V mitochondrial respiratory chain ATPAF2 subunit deficiency (ATPAF2 deficiency) [MIM:604273]; also called ATP synthase deficiency or ATPase deficiency. ATPAF2 deficiency seems to be an early presenting disease in which lactic acidosis, dysmorphic features, and methyl glutaconic aciduria can be major clues in the diagnosis. Dysmorphic features include a large mouth, prominent nasal bridge, micrognathia, rocker-bottom feet and flexion contractures of the limbs associated with camptodactyly. Patients are hypertonic and have an enlarged liver, hypoplastic kidneys and elevated lactate levels in urine, plasma and cerebro spinal fluid (CSF).

Product Properties

Isotype	Rabbit IgG
SDS-PAGE	150 kDa
Purification Method	Immunogen affinity purified
Form	Liquid
Concentration	1.0 mg/mL
Storage Temp	Store at -20°C,Avoid repeated freezing and thawing
Shipped In	Ice chest + Ice pads
Stability And Storage	Store at 4°C short term (1-2 weeks). Store at -20°C long term (12 months). Upon delivery aliquot. Avoid freeze/thaw cycle.

Application

Dilution info

1/500-1/2000

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Basic Description